MCFD2 Rabbit anti-Human, Mouse, Rat, Polyclonal, Proteintech

Rabbit Polyclonal Antibody

Brand:  Proteintech 13068-1-AP-20UL

Product Code. 16861104

Description

Multiple coagulation factor deficiency protein 2 (MCFD2) is localized in the endoplasmic reticulum-Golgi intermediate compartment (ERGIC) through a direct, calcium-dependent interaction with LMAN1. The MCFD2-LMAN1 complex forms a specific cargo receptor for the transport of selected proteins from the endoplasmic reticulum to the Golgi apparatus. Mutations in the MCFD2 gene may cause of factor V and factor VIII combined deficiency (F5F8D). F5F8D is an autosomal recessive human bleeding disorder characterized by the reduction of both clotting proteins.

Specifications

• Antigen: MCFD2
• Classification: Polyclonal
• Conjugate: Unconjugated
• Gene: MCFD2
• Gene Alias: LMAN1IP, MCFD2, SDNSF
• Host Species: Rabbit
• Purification Method: Antigen Affinity Chromatography
• Regulatory Status: RUO
• Gene ID (Entrez): 193813, 246117, 90411
• Content And Storage: -20°C
• Form: Liquid

• Applications: Immunofluorescence, Immunocytochemistry
• Concentration: 0.18 mg/mL
• Formulation: PBS with 50% glycerol and 0.1% sodium azide; pH 7.3
• Gene Accession No.: Q8K5B2, Q8K5B3, Q8NI22
• Gene Symbols: MCFD2
• Immunogen: MCFD2 Fusion Protein Ag3768
• Quantity: 20 μL
• Primary or Secondary: Primary
• Target Species: Rat, Human, Mouse
• Product Type: Antibody
• Isotype: IgG