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  6. Invitrogen™ GAA Recombinant Rabbit Monoclonal Antibody (K01_3K03)

Invitrogen™ GAA Recombinant Rabbit Monoclonal Antibody (K01_3K03)

Product Code. 30829632
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100 μL
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30829632 50 μL
30830042 100 μL
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Product Code. 30829632 Supplier Invitrogen™ Supplier No. MA565784

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Description

Rabbit Recombinant Monoclonal Antibody

GAA Recombinant Monoclonal Antibody for Western Blot

This gene encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Three transcript variants encoding the same protein have been found for this gene.
TRUSTED_SUSTAINABILITY

Specifications

Antigen GAA
Applications Western Blot
Classification Recombinant Monoclonal
Clone K01_3K03
Concentration 0.8 mg/mL
Conjugate Unconjugated
Formulation 50mM tris glycine with 0.05% BSA, 40% glycerol, 150mM NaCl and 0.01% sodium azide; pH 7.4
Gene Gaa
Gene Accession No. P10253, P70699, Q6P7A9
Gene Alias 70 kDa lysosomal alpha-glucosidase; 76 kDa lysosomal alpha-glucosidase; acid (Pompe disease, glycogen storage disease type II); acid alpha-glucosidase; acid maltase; Aglucosidase alfa; E430018M07Rik; Gaa; glucosidase alpha, acid; glucosidase, alpha, acid; glucosidase, alpha; acid (Pompe disease, glycogen storage disease type II); LYAG; Lysosomal alpha-glucosidase
Gene Symbols Gaa
Host Species Rabbit
Immunogen Peptide.
Purification Method Affinity chromatography
Quantity 50 μL
Regulatory Status RUO
Primary or Secondary Primary
Gene ID (Entrez) 14387, 2548, 367562
Target Species Human, Mouse, Rat
Content And Storage Maintain refrigerated at 2-8°C for up to 1 month. For long term storage store at -20°C
Product Type Antibody
Form Liquid
Isotype IgG
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