GAA Rabbit anti-Human, Mouse, Rat, Polyclonal, Proteintech

Rabbit Polyclonal Antibody

Product Code	Brand	Quantity
16832984	Proteintech 14367-1-AP-20UL	20 μL
16822984	Proteintech 14367-1-AP-150UL	150 μL

Description

This gene encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe′s disease, which is an autosomal recessive disorder with a broad clinical spectrum. Three transcript variants encoding the same protein have been found for this gene.

Specifications

• Antigen: GAA
• Applications: Immunoprecipitation, Immunohistochemistry (Paraffin), Western Blot
• Conjugate: Unconjugated
• Host Species: Rabbit
• Target Species: Human, Rat, Mouse
• Gene Accession No.: P10253, P70699, Q6P7A9
• Gene ID (Entrez): 14387, 2548, 367562
• Immunogen: GAA Fusion Protein Ag5690
• Primary or Secondary: Primary
• Content And Storage: -20°C
• Gene: GAA

• Concentration: 0.16 mg/mL
• Classification: Polyclonal
• Form: Liquid
• Regulatory Status: RUO
• Formulation: PBS with 50% glycerol and 0.02% sodium azide; pH 7.3
• Gene Alias: Acid maltase, Aglucosidase alfa, GAA, glucosidase, alpha; acid, LYAG, Lysosomal alpha glucosidase
• Gene Symbols: Gaa
• Isotype: IgG
• Purification Method: Antigen Affinity Chromatography
• Product Type: Antibody