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Invitrogen™ ETFDH Polyclonal Antibody

Rabbit Polyclonal Antibody
Brand: Invitrogen™ PA5109695
Description
Immunogen sequence: LVALGLVVGL DYQNPYLSPF REFQRWKHHP SIRPTLEGGK RIAYGARALN EGGFQSIPKL TFPGGLLIGC SPGFMNVPKI KGTHTAMKSG ILAAESIFNQ LTSENLQSKT IGLHVTEYED NLKNSWVWKE LYSVRNIRPS CHGVLGVYGG MIYTGIFYWI LRGMEPWTLK HKGSDFERLK PAKDCTPIEY PKPDGQISFD LLSSVALSGT NHEHDQPAHL TLRDDSIPVN RNLSIYDGPE QRFCPAGVYE FVPVEQGDGF RLQINAQNCV HCKTCDIKDP SQNINWVVPE GGGGPAYNGM.
Electron-transferring-flavoprotein dehydrogenase in the inner mitochondrial membrane accepts electrons from electron-transfer flavoprotein which is located in the mitochondrial matrix and reduces ubiquinone in the mitochondrial membrane. The protein is synthesized as a 67-kDa precursor which is targeted to mitochondria and processed in a single step to a 64-kDa mature form located in the mitochondrial membrane. Deficiency in electron-transferring-flavoprotein dehydrogenase have been demonstrated in some patients with type II glutaricacidemia.
Specifications
| ETFDH | |
| Polyclonal | |
| Unconjugated | |
| Etfdh | |
| 0610010I20Rik; AV001013; electron transfer flavoprotein dehydrogenase; electron transfer flavoprotein-ubiquinone oxidoreductase, mitochondrial; electron transferring flavoprotein dehydrogenase; electron transferring flavoprotein, dehydrogenase; electron-transferring-flavoprotein dehydrogenase; ETF dehydrogenase; Etfdh; ETFQO; ETF-QO; ETF-ubiquinone oxidoreductase; MADD | |
| Rabbit | |
| Affinity Chromatography | |
| RUO | |
| 2110, 295143, 66841 | |
| -20°C, Avoid Freeze/Thaw Cycles | |
| Liquid |
| ELISA, Western Blot | |
| 0.92 mg/mL | |
| PBS with 50% glycerol and 0.02% sodium azide; pH 7.3 | |
| Q16134, Q6UPE1, Q921G7 | |
| Etfdh | |
| Recombinant fusion protein containing a sequence corresponding to amino acids 318-617 of human ETFDH (NP_004444.2). | |
| 100 μL | |
| Primary | |
| Human, Mouse, Rat | |
| Antibody | |
| IgG |
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