DCBLD2 Rabbit anti-Human, Mouse, Rat, Polyclonal, Proteintech

Rabbit Polyclonal Antibody

Brand:  Proteintech 13168-1-AP-20UL

Product Code. 16841244

Description

This protein is a key enzyme in the catabolic pathway of odd-chain fatty acids, isoleucine, threonine, methionine, and valine. It is probably a dodecamer composed of six biotin-containing alpha subunits and six beta subunits. The protein is located in the mitochondrial matrix. Defects in PCCA are the cause o fpropionic acidemia type I (PA-1) [MIM:606054]. PA-1 is a life-threatening disease characterized by episodic vomiting, lethargy and ketosis, neutropenia, periodic thrombocytopenia, hypogammaglobulinemia, develop-mental retardation, and intolerance to protein.

Specifications

• Antigen: DCBLD2
• Classification: Polyclonal
• Conjugate: Unconjugated
• Gene: DCBLD2
• Gene Alias: CLCP1, DCBLD2, ESDN
• Host Species: Rabbit
• Purification Method: Antigen Affinity Chromatography
• Regulatory Status: RUO
• Gene ID (Entrez): 131566, 155696, 73379
• Content And Storage: -20°C
• Form: Liquid

• Applications: Western Blot, Immunoprecipitation
• Concentration: 0.18 mg/mL
• Formulation: PBS with 50% glycerol and 0.02% sodium azide; pH 7.3
• Gene Accession No.: Q91ZV2, Q91ZV3, Q96PD2
• Gene Symbols: Dcbld2
• Immunogen: DCBLD2 Fusion Protein Ag3821
• Quantity: 20 μL
• Primary or Secondary: Primary
• Target Species: Human, Rat, Mouse
• Product Type: Antibody
• Isotype: IgG