Invitrogen™ DCBLD2 Polyclonal Antibody

Rabbit Polyclonal Antibody

Brand:  Invitrogen™ PA14270

Product Code. 11598800

Description

PA1-4270 detects ESDN from human, mouse and rat samples. PA1-4270 has been successfully used in Western blot procedures. PA1-4270 immunizing peptide corresponds to amino acid residues 399-416 from mouse and rat ESDN protein.

This protein is a key enzyme in the catabolic pathway of odd-chain fatty acids, isoleucine, threonine, methionine, and valine. It is probably a dodecamer composed of six biotin-containing alpha subunits and six beta subunits. The protein is located in the mitochondrial matrix. Defects in PCCA are the cause o fpropionic acidemia type I (PA-1) [MIM:606054]. PA-1 is a life-threatening disease characterized by episodic vomiting, lethargy and ketosis, neutropenia, periodic thrombocytopenia, hypogammaglobulinemia, develop-mental retardation, and intolerance to protein.

Specifications

• Antigen: DCBLD2
• Classification: Polyclonal
• Conjugate: Unconjugated
• Gene: DCBLD2
• Gene Alias: 1700055P21Rik; AW146002; CLCP1; coagulation factor V/VIII-homology domains protein 1; CUB, LCCL and coagulation factor V/VIII-homology domains protein 1; DCBLD2; discoidin; discoidin, CUB and LCCL domain containing 2; discoidin, CUB and LCCL domain-containing protein 2; Endothelial and smooth muscle cell-derived neuropilin-like protein; ESDN
• Host Species: Rabbit
• Purification Method: Antigen affinity chromatography
• Regulatory Status: RUO
• Gene ID (Entrez): 131566, 155696, 73379
• Content And Storage: -20°C, Avoid Freeze/Thaw Cycles
• Form: Liquid

• Applications: Western Blot
• Concentration: 1 mg/mL
• Formulation: PBS with 0.02% sodium azide
• Gene Accession No.: Q91ZV2, Q91ZV3, Q96PD2
• Gene Symbols: DCBLD2
• Immunogen: Synthetic Peptide: Q(399) D K I F Q G N K D Y H K D V R N N(416).
• Quantity: 100 μg
• Primary or Secondary: Primary
• Target Species: Human, Mouse, Rat
• Product Type: Antibody
• Isotype: IgG