Alpha galactosidase A Mouse anti-Human, Clone: 2B2C5, Proteintech

Mouse Monoclonal Antibody

Brand:  Proteintech 66121-1-IG-20UL

Product Code. 16897705

Description

This gene encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predomitly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties.

Specifications

• Antigen: Alpha galactosidase A
• Classification: Monoclonal
• Concentration: 2.39 mg/mL
• Formulation: PBS with 50% glycerol and 0.02% sodium azide; pH 7.3
• Gene Accession No.: P06280
• Gene Symbols: GLA
• Immunogen: Alpha galactosidase A Fusion Protein Ag7505
• Quantity: 20 μL
• Primary or Secondary: Primary
• Target Species: Human
• Product Type: Antibody
• Isotype: IgG2a

• Applications: Immunofluorescence, Western Blot, Immunohistochemistry (Paraffin), Immunocytochemistry
• Clone: 2B2C5
• Conjugate: Unconjugated
• Gene: GLA
• Gene Alias: Alpha galactosidase A, galactosidase, alpha
• Host Species: Mouse
• Purification Method: Protein A
• Regulatory Status: RUO
• Gene ID (Entrez): 2717
• Content And Storage: -20°C
• Form: Liquid